Erdheim disease

Erdheim disease --> cystic medial necrosis

Loss of elastic and muscle fibres in the aortic media, with accumulation of mucopolysaccharide, sometimes in cystlike spaces between the fibres; a disease of unknown cause, which may be inherited and which predisposes to dissecting aneurysms.

Synonym: erdheim disease, medionecrosis aortae idiopathica cystica, medionecrosis of the aorta, mucoid medial degeneration.

Please contribute to this project, if you have more information about this term feel free to edit this page

This page was last modified on 3 October 2005, at 21:16. This page has been accessed 769 times. 
What links here | Related changes | Permanent link